Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center for Pediatric Genomic Medicine, |
RCV000438755 | SCV000511307 | uncertain significance | not provided | 2016-09-15 | criteria provided, single submitter | clinical testing | Converted during submission to Uncertain significance. |
Fulgent Genetics, |
RCV000764157 | SCV000895154 | uncertain significance | Tenorio syndrome | 2018-10-31 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000764157 | SCV000953315 | uncertain significance | Tenorio syndrome | 2018-08-20 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0"). This variant has not been reported in the literature in individuals with RNF125-related disease. ClinVar contains an entry for this variant (Variation ID: 377122). This variant is present in population databases (rs751589349, ExAC 0.003%). This sequence change replaces proline with leucine at codon 31 of the RNF125 protein (p.Pro31Leu). The proline residue is highly conserved and there is a moderate physicochemical difference between proline and leucine. |
Ce |
RCV000438755 | SCV005051390 | likely benign | not provided | 2024-05-01 | criteria provided, single submitter | clinical testing | RNF125: BS1 |