Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
KCCC/NGS Laboratory, |
RCV003315493 | SCV004015252 | uncertain significance | Pheochromocytoma | 2023-07-07 | criteria provided, single submitter | clinical testing | This sequence change replaces proline with leucine at codon 87 of the TMEM127 protein. The proline residue is moderately conserved and there is a large physicochemical difference between proline and leucine. This variant is not present in population databases (gnomAD). This variant has not been reported in the literature in individuals with TMEM127-related disease. ClinVar does not contain an entry for this variant. In silico predictions show SIFT: "damaging"; and PolyPhen-2: "tolerated". Therefore, it has been classified as a Variant of Uncertain Significance. |