Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001882258 | SCV002163000 | uncertain significance | not provided | 2021-05-18 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This sequence change falls in intron 9 of the RNF31 gene. It does not directly change the encoded amino acid sequence of the RNF31 protein. RNA analysis indicates that this variant induces altered splicing and likely results in a shortened protein product. This variant is not present in population databases (ExAC no frequency). This variant has been observed in individual(s) with common variable immune deficiency (PMID: 30936877). Nucleotide substitutions within the consensus splice site are a relatively common cause of aberrant splicing (PMID: 17576681, 9536098). Studies have shown that this variant is associated with skipping of exon 9 but is expected to preserve the integrity of the reading frame (PMID: 30936877). |
OMIM | RCV003444156 | SCV004171229 | pathogenic | Immunodeficiency 115 with autoinflammation | 2023-11-28 | no assertion criteria provided | literature only |