Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000233098 | SCV000290421 | benign | Fanconi anemia | 2024-01-31 | criteria provided, single submitter | clinical testing | |
Genetic Services Laboratory, |
RCV001820756 | SCV002071251 | uncertain significance | not specified | 2020-04-24 | criteria provided, single submitter | clinical testing | DNA sequence analysis of the FANCL gene demonstrated a sequence change, c.963T>A, in exon 12 that results in an amino acid change, p.Asp321Glu. This sequence change does not appear to have been previously described in patients with FANCL-related disorders and has been described in the gnomAD database with a population frequency of 0.54% in the African subpopulation; however, it has not been observed in homozygous state in any individuals (dbSNP rs140088149). The p.Asp321Glu change affects a highly conserved amino acid residue located in a domain of the FANCL protein that is not known to be functional. In-silico pathogenicity prediction tools (SIFT, PolyPhen2, Align GVGD, REVEL) provide contradictory results for the p.Asp321Glu substitution. Due to these contrasting evidences and the lack of functional studies, the clinical significance of the p.Asp321Glu change remains unknown at this time. |
Sema4, |
RCV000233098 | SCV002527302 | likely benign | Fanconi anemia | 2020-12-18 | criteria provided, single submitter | curation | |
KCCC/NGS Laboratory, |
RCV003316291 | SCV004015684 | likely benign | Fanconi anemia complementation group L | 2023-07-07 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV003955361 | SCV004776130 | likely benign | FANCL-related disorder | 2021-06-23 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |