Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004797955 | SCV005419553 | likely pathogenic | not provided | 2024-05-22 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 33417887) |
OMIM | RCV001837163 | SCV002097581 | pathogenic | Charcot-Marie-Tooth disease, demyelinating, IIA 1I | 2022-06-17 | no assertion criteria provided | literature only |