Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000520399 | SCV000618793 | uncertain significance | not provided | 2017-07-01 | criteria provided, single submitter | clinical testing | The K354E variant in the WDR11 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The K354E variant is observed in 1/66738 (0.0014%) alleles from individuals of non-Finnish European background, in the ExAC dataset (Lek et al., 2016). The K354E variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. This substitution occurs within the WD 3 repeat domain, at a position that is conserved across species. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. We interpret K354E as a variant of uncertain significance. |