Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001881359 | SCV002152511 | uncertain significance | Combined oxidative phosphorylation defect type 17 | 2021-07-08 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. This variant has not been reported in the literature in individuals affected with ELAC2-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change falls in intron 6 of the ELAC2 gene. It does not directly change the encoded amino acid sequence of the ELAC2 protein. |