Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics, |
RCV003994608 | SCV004812446 | benign | Autosomal recessive spinocerebellar ataxia 17 | 2023-05-04 | criteria provided, single submitter | clinical testing | European Non-Finnish population allele frequency is 2.395% (rs35490714, 881/25114 alleles, 13 homozygotes in gnomAD v2.1). Based on the classification scheme RMH Modified ACMG/AMP Guidelines v1.5.1, this variant is classified as BENIGN. Following criteria are met: BA1 |
Prevention |
RCV003973925 | SCV004789852 | benign | CWF19L1-related disorder | 2019-09-10 | no assertion criteria provided | clinical testing | This variant is classified as benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |