Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001291711 | SCV001480296 | pathogenic | Autosomal recessive spinocerebellar ataxia 17 | 2019-09-27 | criteria provided, single submitter | clinical testing | The c.708+294_1044+1540del, a novel copy number deletion variant encompassing exons 8, 9,and 10 of the CWF19L1 gene is predicted to result in an in-frame deletion of 112 amino acids (p.Tyr237_His348del) [PMID: 18000842]. This variant is not present in gnomAD database and has not been reported in the literature in individuals with a CWF19L1-related disease. Splice site mutation resulting in exon 9 skipping of CWF19L1 has been reported for the patient with autosomal recessive spinocerebellar ataxia-17 [PMID: 25361784]. Based on the available evidence, the c.708+294_1044+1540del variant in the CWF19L1 gene is classified as pathogenic. |