Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000199743 | SCV000252072 | likely benign | not specified | 2013-05-05 | criteria provided, single submitter | clinical testing | The variant is found in MITONUC-MITOP panel(s). |
Labcorp Genetics |
RCV001853192 | SCV002172342 | uncertain significance | not provided | 2022-07-09 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Tolerated"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. ClinVar contains an entry for this variant (Variation ID: 214971). This sequence change replaces alanine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 532 of the PDP1 protein (p.Ala532Val). This variant is present in population databases (rs768767735, gnomAD 0.03%). This variant has not been reported in the literature in individuals affected with PDP1-related conditions. |