Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000731730 | SCV000859579 | uncertain significance | not provided | 2018-02-06 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000731730 | SCV002567487 | uncertain significance | not provided | 2022-02-19 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV000731730 | SCV003498170 | uncertain significance | not provided | 2022-10-04 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 596029). This variant has not been reported in the literature in individuals affected with VPS33B-related conditions. This variant is present in population databases (no rsID available, gnomAD 0.03%). This sequence change replaces glutamic acid, which is acidic and polar, with lysine, which is basic and polar, at codon 213 of the VPS33B protein (p.Glu213Lys). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt VPS33B protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Prevention |
RCV003392570 | SCV004119947 | uncertain significance | VPS33B-related disorder | 2023-08-05 | criteria provided, single submitter | clinical testing | The VPS33B c.637G>A variant is predicted to result in the amino acid substitution p.Glu213Lys. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.028% of alleles in individuals of African descent in gnomAD (http://gnomad.broadinstitute.org/variant/15-91550243-C-T). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |
Fulgent Genetics, |
RCV005010739 | SCV005643402 | uncertain significance | Arthrogryposis, renal dysfunction, and cholestasis 1; Keratoderma-ichthyosis-deafness syndrome, autosomal recessive; Cholestasis, progressive familial intrahepatic, 12 | 2024-04-29 | criteria provided, single submitter | clinical testing |