Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002412170 | SCV002670041 | uncertain significance | Cardiovascular phenotype | 2022-04-03 | criteria provided, single submitter | clinical testing | The p.R261S variant (also known as c.783G>T), located in coding exon 7 of the PRDM5 gene, results from a G to T substitution at nucleotide position 783. The arginine at codon 261 is replaced by serine, an amino acid with dissimilar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003130711 | SCV003809843 | uncertain significance | Brittle cornea syndrome 2 | 2022-03-28 | criteria provided, single submitter | clinical testing |