Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003528939 | SCV004260056 | uncertain significance | 2-aminoadipic 2-oxoadipic aciduria | 2023-10-09 | criteria provided, single submitter | clinical testing | This sequence change affects the initiator methionine of the DHTKD1 mRNA. The next in-frame methionine is located at codon 108. This variant is present in population databases (rs760903542, gnomAD 0.003%). Disruption of the initiator codon has been observed in individual(s) with 2-aminoadipic 2-oxoadipic aciduria (PMID: 23141293). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |