Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000623083 | SCV000741192 | uncertain significance | Inborn genetic diseases | 2015-11-19 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001855294 | SCV002214171 | uncertain significance | 2-aminoadipic 2-oxoadipic aciduria | 2021-08-30 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 520868). This variant has not been reported in the literature in individuals affected with DHTKD1-related conditions. This variant is present in population databases (rs780598300, ExAC 0.05%). This sequence change replaces serine with leucine at codon 209 of the DHTKD1 protein (p.Ser209Leu). The serine residue is moderately conserved and there is a large physicochemical difference between serine and leucine. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |