Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV000417081 | SCV002023552 | likely pathogenic | Hypermanganesemia with dystonia, polycythemia, and cirrhosis | 2021-09-02 | criteria provided, single submitter | clinical testing | |
3billion, |
RCV000417081 | SCV002572886 | uncertain significance | Hypermanganesemia with dystonia, polycythemia, and cirrhosis | 2022-09-01 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.60; 3Cnet: 0.47). Same nucleotide change resulting in same amino acid change has been previously reported to be associated with SLC30A10 -related disorder (ClinVar ID: VCV000375609 / PMID: 27117033). However, the evidence of pathogenicity is insufficient at this time. Therefore, this variant is classified as uncertain significance according to the recommendation of ACMG/AMP guideline. |
Gene |
RCV000417081 | SCV000494641 | not provided | Hypermanganesemia with dystonia, polycythemia, and cirrhosis | no assertion provided | literature only |