Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004764880 | SCV005374801 | uncertain significance | Spinocerebellar ataxia type 42 | criteria provided, single submitter | clinical testing | The observed missense c.1364C>T(p.Ser455Phe) variant in CACNA1G gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Ser455Phe variant is absent in gnomAD Exomes database. This variant has not been submitted to the ClinVar database. Multiple lines of computational evidence (Polyphen - Benign, SIFT - Tolerated and MutationTaster -polymorphism) predict no damaging effect on protein structure and function for this variant. The reference amino acid in CACNA1G is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Ser at position 455 is changed to a Phe changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as Uncertain Significance (VUS). |