Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute for Human Genetics and Genomic Medicine, |
RCV001543133 | SCV001749121 | uncertain significance | Spinocerebellar ataxia type 42 | 2021-07-12 | criteria provided, single submitter | clinical testing | The sequence variant NM_018896.4:c.532G>A, p.(Ala178Thr) in CACNA1G is absent from databases and has not been reported in the literature. It was found in 3 affected members in 2 generations in a family which was initially described as having CMT. However, one of the carriers shows a broader phenotype with saccadic pursuit and mild ataxia. There is no information on the exact clinical picture of the relatives. We therefore classified this variant as a "variant of uncertain significance". |