Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001839145 | SCV002099071 | uncertain significance | Spinocerebellar ataxia 42, early-onset, severe, with neurodevelopmental deficits | 2021-05-18 | criteria provided, single submitter | clinical testing | The inherited heterozygous c.5906T>C, p.Leu1969Pro variant in CACNA1G has not been reported in the literature. This variant is absent in the gnomAD v3.1 database, indicating a rare allele, and in silico tools predict a conflicting evidence of pathogenicity. Based on the available evidence, the inherited c.5906T>C, p.Leu1969Pro variant in the CACNA1G gene is classified as a variant of uncertain significance. |