Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ISTH- |
RCV002222149 | SCV002499626 | uncertain significance | Thrombocytopenia 4 | criteria provided, single submitter | clinical testing | ||
Labcorp Genetics |
RCV003774641 | SCV004634536 | uncertain significance | not provided | 2023-02-08 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. ClinVar contains an entry for this variant (Variation ID: 1676752). This missense change has been observed in individual(s) with macrothrombocytopenia (PMID: 34355501). This variant is not present in population databases (gnomAD no frequency). This sequence change replaces leucine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 33 of the CYCS protein (p.Leu33Val). |