Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV005065364 | SCV005690632 | uncertain significance | Pseudohypoaldosteronism type 2C | 2023-06-22 | criteria provided, single submitter | clinical testing | The missense c.2803C>A (p.Pro935Thr) variant in WNK1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Pro935Thr variant is absent in gnomAD Exomes. This variant has not been submitted to the ClinVar database. Multiple lines of computational evidence (Polyphen - Possibly damaging, SIFT - Tolerated and MutationTaster - Disease causing) predicts conflicting evidence on protein structure and function for this variant. The reference amino acid at this position on WNK1 gene is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Pro at position 935 is changed to a Thr changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as Variant of Uncertain Significance (VUS). |