Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002903455 | SCV003252869 | uncertain significance | not provided | 2024-10-29 | criteria provided, single submitter | clinical testing | This sequence change replaces asparagine, which is neutral and polar, with aspartic acid, which is acidic and polar, at codon 814 of the ADAMTSL4 protein (p.Asn814Asp). This variant is present in population databases (rs587653896, gnomAD 0.1%). This variant has not been reported in the literature in individuals affected with ADAMTSL4-related conditions. ClinVar contains an entry for this variant (Variation ID: 2044134). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) indicates that this missense variant is not expected to disrupt ADAMTSL4 protein function with a negative predictive value of 80%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV002903456 | SCV003735551 | uncertain significance | Inborn genetic diseases | 2022-06-24 | criteria provided, single submitter | clinical testing | The c.2440A>G (p.N814D) alteration is located in exon 15 (coding exon 13) of the ADAMTSL4 gene. This alteration results from a A to G substitution at nucleotide position 2440, causing the asparagine (N) at amino acid position 814 to be replaced by an aspartic acid (D). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Genome- |
RCV003340551 | SCV004049626 | uncertain significance | Ectopia lentis et pupillae | 2023-04-11 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV003340550 | SCV004049628 | uncertain significance | Ectopia lentis 2, isolated, autosomal recessive | 2023-04-11 | criteria provided, single submitter | clinical testing |