Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001355068 | SCV002957882 | likely benign | not provided | 2024-08-01 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003284252 | SCV003970360 | likely benign | Inborn genetic diseases | 2023-03-31 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Ce |
RCV001355068 | SCV004131419 | likely benign | not provided | 2024-07-01 | criteria provided, single submitter | clinical testing | MAGEL2: BS1 |
Breakthrough Genomics, |
RCV001355068 | SCV005193645 | uncertain significance | not provided | criteria provided, single submitter | not provided | ||
Department of Pathology and Laboratory Medicine, |
RCV001355068 | SCV001549836 | uncertain significance | not provided | no assertion criteria provided | clinical testing | The MAGEL2 p.Pro14Gln variant was not identified in the literature nor was it identified in ClinVar. The variant was identified in dbSNP (ID: rs769643348) and LOVD 3.0 (classified as a VUS). The variant was identified in control databases in 68 of 134210 chromosomes at a frequency of 0.0005067 (Genome Aggregation Database March 6, 2019, v2.1.1). The variant was observed in the following populations: Other in 8 of 4052 chromosomes (freq: 0.001974), European (non-Finnish) in 59 of 61438 chromosomes (freq: 0.00096) and African in 1 of 15712 chromosomes (freq: 0.000064), but was not observed in the Latino, Ashkenazi Jewish, East Asian, European (Finnish) or South Asian populations. Computational analyses (PolyPhen-2, BLOSUM, MutationTaster) suggest that the variant will impact to the protein; however this information is not predictive enough to assume pathogenicity. In summary, based on the above information the clinical significance of this variant cannot be determined with certainty at this time. This variant is classified as a variant of uncertain significance. |