Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Diagnostics Services |
RCV004798112 | SCV005419244 | uncertain significance | Achromatopsia 3 | 2024-11-14 | criteria provided, single submitter | clinical testing | The c.1096_1104del variant is not present in publicly available population databases like 1000 Genomes, EVS, ExAC, gnomAD and our in-house exome database. The variant is present in the Indian Exome Database at a low frequency. This variant has neither been published in literature with CNGB3-related conditions nor reported to the clinical databases like ClinVar, Human Gene Mutation Database (HGMD) or OMIM, in any affected individuals. Predictions from different in-silico pathogenicity prediction programs are inconclusive. This variant is located in a non-repeat region of the gene that causes change in protein length by in-frame deletion of 3 amino acids. |