Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center for Genomic Medicine, |
RCV003993610 | SCV004809650 | likely pathogenic | Congenital factor VII deficiency | 2024-04-04 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004690502 | SCV005184662 | uncertain significance | not specified | 2024-05-14 | criteria provided, single submitter | clinical testing | Variant summary: F7 c.262C>T (p.Arg88Trp) results in a non-conservative amino acid change located in the Gamma-carboxyglutamic acid-rich (GLA) domain (IPR000294) of the encoded protein sequence. Five of five in-silico tools predict a damaging effect of the variant on protein function. The variant was absent in 167586 control chromosomes (gnomAD). The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.262C>T in individuals affected with Congenital factor VII deficiency and no experimental evidence demonstrating its impact on protein function have been reported. No submitters have cited clinical-significance assessments for this variant to ClinVar. Based on the evidence outlined above, the variant was classified as uncertain significance. |
Mayo Clinic Laboratories, |
RCV004790652 | SCV005409655 | uncertain significance | not provided | 2024-04-26 | criteria provided, single submitter | clinical testing | PM1_supporting, PM2_moderate |