Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Breakthrough Genomics, |
RCV004596705 | SCV005088875 | likely pathogenic | Congenital factor VII deficiency | 2021-01-23 | criteria provided, single submitter | clinical testing | This variant is predicted to cause a frameshift and consequent premature termination of the protein (p. Leu347ArgfsTer19) and this will likely result in loss-of-function. The variant seems to be a novel variant, as it has not been previously reported in population or public databases or in the literature. However, in the ClinVar database another truncating variants lying downstream of the variant, has been previously reported as ‘likely pathogenic’ in the context of Factor VII deficiency and abnormal bleeding. |