Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002632235 | SCV003502787 | benign | not provided | 2023-12-02 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002603294 | SCV003613807 | uncertain significance | Inborn genetic diseases | 2022-02-03 | criteria provided, single submitter | clinical testing | The c.1295G>T (p.R432L) alteration is located in exon 10 (coding exon 10) of the KCNQ5 gene. This alteration results from a G to T substitution at nucleotide position 1295, causing the arginine (R) at amino acid position 432 to be replaced by a leucine (L). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003994504 | SCV004813802 | uncertain significance | not specified | 2024-02-08 | criteria provided, single submitter | clinical testing | Variant summary: KCNQ5 c.1295G>T (p.Arg432Leu) results in a non-conservative amino acid change in the encoded protein sequence. Three of five in-silico tools predict a damaging effect of the variant on protein function. The variant allele was found at a frequency of 6.9e-06 in 1454212 control chromosomes (i.e. in 10 carriers) in the gnomAD database v4.0 dataset. To our knowledge, no occurrence of c.1295G>T in individuals affected with Intellectual Disability, Autosomal Dominant 46 and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 2184435). Based on the evidence outlined above, the variant was classified as VUS-possibly benign. |