Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000500550 | SCV000594849 | uncertain significance | not specified | 2017-03-31 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000913044 | SCV001058182 | likely benign | not provided | 2018-03-29 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000500550 | SCV005203292 | uncertain significance | not specified | 2024-07-08 | criteria provided, single submitter | clinical testing | Variant summary: FMN2 c.4068T>C (p.Val1356Val) alters a conserved nucleotide located close to a canonical splice site and therefore could affect mRNA splicing, leading to a significantly altered protein sequence. Consensus agreement among computation tools predict no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. The variant allele was found at a frequency of 0.00015 in 250484 control chromosomes. This frequency is not significantly higher than estimated for a pathogenic variant in FMN2 causing Intellectual Disability, Autosomal Recessive 47, allowing no conclusion about variant significance. To our knowledge, no occurrence of c.4068T>C in individuals affected with Intellectual Disability, Autosomal Recessive 47 and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 435234). Based on the evidence outlined above, the variant was classified as uncertain significance. |
Prevention |
RCV003902773 | SCV004721726 | likely benign | FMN2-related disorder | 2021-01-20 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |