Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003388733 | SCV004100482 | likely pathogenic | Pancytopenia-developmental delay syndrome | criteria provided, single submitter | clinical testing | The splice acceptor variant c.1948-1G>A in ERCC6L2 (NM_020207.7) has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The c.1948-1G>A variant is novel (not in any individuals) in gnomAD Exomes and is novel (not in any individuals) in 1000 Genomes. This variant mutates a splice-acceptor sequence, potentially resulting in exon skipping and the production of abnormal proteins. For these reasons, this variant has been classified as Likely Pathogenic. |