Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001066918 | SCV001231942 | pathogenic | Dilated cardiomyopathy 1O | 2024-10-04 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Met977Lysfs*11) in the ABCC9 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in ABCC9 are known to be pathogenic (PMID: 31575858, 38217872). This variant is present in population databases (no rsID available, gnomAD 0.0009%). This variant has not been reported in the literature in individuals affected with ABCC9-related conditions. ClinVar contains an entry for this variant (Variation ID: 860588). For these reasons, this variant has been classified as Pathogenic. |
Ai |
RCV002223985 | SCV002502488 | uncertain significance | not provided | 2021-12-21 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV003333130 | SCV004041039 | uncertain significance | Atrial fibrillation, familial, 12 | 2023-04-20 | criteria provided, single submitter | clinical testing |