Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001175594 | SCV001339241 | benign | not specified | 2020-03-02 | criteria provided, single submitter | clinical testing | Variant summary: ABCC9 c.817-18dupT alters a non-conserved nucleotide located close to a canonical splice site and therefore could affect mRNA splicing, leading to a significantly altered protein sequence. 4/4 computational tools predict no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. The variant allele was found at a frequency of 0.039 in 103156 control chromosomes in the gnomAD database, including 13 homozygotes. The observed variant frequency is approximately 1555-fold the estimated maximal expected allele frequency for a pathogenic variant in ABCC9 causing Cardiomyopathy phenotype (2.5e-05), strongly suggesting that the variant is benign. To our knowledge, no occurrence of c.817-18dupT in individuals affected with Cardiomyopathy and no experimental evidence demonstrating its impact on protein function have been reported. No clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014. Based on the evidence outlined above, the variant was classified as benign. |
Labcorp Genetics |
RCV002068136 | SCV002368653 | benign | Dilated cardiomyopathy 1O | 2024-01-31 | criteria provided, single submitter | clinical testing | |
Clinical Genetics, |
RCV001175594 | SCV001920955 | benign | not specified | no assertion criteria provided | clinical testing | ||
Genome Diagnostics Laboratory, |
RCV001175594 | SCV001928103 | benign | not specified | no assertion criteria provided | clinical testing | ||
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV001175594 | SCV001967973 | benign | not specified | no assertion criteria provided | clinical testing | ||
Institute of Human Genetics, |
RCV004596414 | SCV005088647 | benign | Hypertrophic cardiomyopathy 2 | no assertion criteria provided | clinical testing |