Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002735453 | SCV003010891 | pathogenic | not provided | 2023-03-03 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 1970672). This sequence change creates a premature translational stop signal (p.His353Alafs*15) in the RARS2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in RARS2 are known to be pathogenic (PMID: 17847012, 22569581, 26083569). The frequency data for this variant in the population databases is considered unreliable, as metrics indicate poor data quality at this position in the gnomAD database. This variant has not been reported in the literature in individuals affected with RARS2-related conditions. For these reasons, this variant has been classified as Pathogenic. |
Baylor Genetics | RCV003464590 | SCV004208477 | pathogenic | Pontocerebellar hypoplasia type 6 | 2024-02-29 | criteria provided, single submitter | clinical testing |