Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001764348 | SCV001997967 | uncertain significance | not provided | 2021-05-07 | criteria provided, single submitter | clinical testing | Not observed at a significant frequency in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; Has not been previously published as pathogenic or benign to our knowledge |
Mendelics | RCV002248649 | SCV002518961 | pathogenic | Pontocerebellar hypoplasia type 6 | 2022-05-04 | criteria provided, single submitter | clinical testing | |
Laboratory of Molecular Genetics, |
RCV000414873 | SCV000493112 | uncertain significance | Severe intellectual deficiency | no assertion criteria provided | clinical testing |