Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001785358 | SCV002026371 | likely pathogenic | Febrile seizures, familial, 11 | 2024-07-24 | criteria provided, single submitter | clinical testing | This variant was identified as compound heterozygous with NM_020361.5:c.127A>G (ClinVar ID: 577800). Functional studies show a significant reduction of CPA6 levels (PMID: 25875328). Criteria applied: PS3, PS4_SUP, PM2_SUP |