Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001306455 | SCV001495827 | uncertain significance | Hypertrophic cardiomyopathy | 2022-11-01 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C15"). ClinVar contains an entry for this variant (Variation ID: 1009029). This variant has not been reported in the literature in individuals affected with JPH2-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces glutamic acid, which is acidic and polar, with lysine, which is basic and polar, at codon 317 of the JPH2 protein (p.Glu317Lys). |
Fulgent Genetics, |
RCV002493608 | SCV002794481 | uncertain significance | Hypertrophic cardiomyopathy 17; Cardiomyopathy, dilated, 2E | 2021-09-14 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003284162 | SCV004004109 | uncertain significance | Cardiovascular phenotype | 2023-06-15 | criteria provided, single submitter | clinical testing | The p.E317K variant (also known as c.949G>A), located in coding exon 2 of the JPH2 gene, results from a G to A substitution at nucleotide position 949. The glutamic acid at codon 317 is replaced by lysine, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |