Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Kasturba Medical College, |
RCV004701242 | SCV005201013 | pathogenic | Hypomyelinating leukodystrophy 2 | 2024-05-09 | criteria provided, single submitter | clinical testing | PVS1 was applied as it is a null variant in a gene with loss of function daises mechanism. The variant is absent in population databases thus, PM2 was applied. The phenotype is specific for a disease with single gene aetiology, thus PP4 was applied. |