Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Consultorio y Laboratorio de Neurogenética, |
RCV001261524 | SCV001424327 | uncertain significance | Hypomyelinating leukodystrophy 2 | criteria provided, single submitter | clinical testing | ||
Molecular Diagnostics Lab, |
RCV001261524 | SCV005187378 | uncertain significance | Hypomyelinating leukodystrophy 2 | 2021-05-24 | criteria provided, single submitter | clinical testing | This missense variant (c.62C>T, p.Thr21Ile) has not been observed in population databases (gnomAD) and has not been reported in the literature. Variant prediction programs suggest a deleterious effect, but no functional studies have been reported. The change was found in the homozygous state in affected twins. |