Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003485858 | SCV003819313 | uncertain significance | Eichsfeld type congenital muscular dystrophy | 2019-03-17 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004961219 | SCV005495036 | uncertain significance | Inborn genetic diseases | 2024-07-09 | criteria provided, single submitter | clinical testing | The c.650T>C (p.L217P) alteration is located in exon 5 (coding exon 5) of the SEPN1 gene. This alteration results from a T to C substitution at nucleotide position 650, causing the leucine (L) at amino acid position 217 to be replaced by a proline (P). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |