Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004687765 | SCV005174570 | uncertain significance | Inborn genetic diseases | 2024-03-20 | criteria provided, single submitter | clinical testing | The c.22G>A (p.E8K) alteration is located in exon 3 (coding exon 1) of the ATP6V0A4 gene. This alteration results from a G to A substitution at nucleotide position 22, causing the glutamic acid (E) at amino acid position 8 to be replaced by a lysine (K). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV005040746 | SCV005666096 | uncertain significance | Renal tubular acidosis, distal, 3, with or without sensorineural hearing loss | 2024-05-25 | criteria provided, single submitter | clinical testing |