Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001320033 | SCV001510803 | uncertain significance | Developmental and epileptic encephalopathy, 34 | 2021-08-12 | criteria provided, single submitter | clinical testing | This sequence change replaces proline with serine at codon 520 of the SLC12A5 protein (p.Pro520Ser). The proline residue is highly conserved and there is a moderate physicochemical difference between proline and serine. This variant is present in population databases (rs113818080, ExAC 0.002%). This missense change has been observed in individual(s) with clinical features of SLC12A5-related conditions (Invitae). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Clinical Genetics Laboratory, |
RCV004697108 | SCV005196837 | uncertain significance | not provided | 2023-04-25 | criteria provided, single submitter | clinical testing |