Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
SIB Swiss Institute of Bioinformatics | RCV000755720 | SCV000883200 | pathogenic | Short-rib thoracic dysplasia 7 with or without polydactyly | 2018-10-15 | criteria provided, single submitter | curation | This variant is interpreted as Pathogenic, for Short-rib thoracic dysplasia 7 with or without polydactyly, autosomal recessive. The following ACMG Tag(s) were applied: PM2 => Absent from controls (or at extremely low frequency if recessive) in Exome Sequencing Project, 1000 Genomes Project, or Exome Aggregation Consortium. PVS1-Strong => PVS1 downgraded in strength to Strong. PS3 => Well-established functional studies show a deleterious effect (https://www.ncbi.nlm.nih.gov/pubmed/28400947). |
University of Washington Center for Mendelian Genomics, |
RCV000851217 | SCV000993468 | likely pathogenic | Short rib-polydactyly syndrome | 2017-03-30 | no assertion criteria provided | research |