Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000908636 | SCV001053411 | likely benign | not provided | 2019-12-31 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003243370 | SCV003937685 | uncertain significance | Inborn genetic diseases | 2023-03-24 | criteria provided, single submitter | clinical testing | The c.3811A>G (p.I1271V) alteration is located in exon 28 (coding exon 28) of the SCAPER gene. This alteration results from a A to G substitution at nucleotide position 3811, causing the isoleucine (I) at amino acid position 1271 to be replaced by a valine (V). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Breakthrough Genomics, |
RCV000908636 | SCV005213259 | likely benign | not provided | criteria provided, single submitter | not provided | ||
Prevention |
RCV004754625 | SCV005358308 | uncertain significance | SCAPER-related disorder | 2024-07-30 | no assertion criteria provided | clinical testing | The SCAPER c.3829A>G variant is predicted to result in the amino acid substitution p.Ile1277Val. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.058% of alleles in individuals of European (Non-Finnish) descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |