Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000413212 | SCV000492064 | uncertain significance | not specified | 2016-11-22 | criteria provided, single submitter | clinical testing | The G546S variant in the FANCM gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The G546S variant was not observed in approximately 6,500 individuals of European and African American ancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benign variant in these populations. The G546S variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. This substitution occurs at a position that is conserved across species, and in silico analysis predicts this variant is probably damaging to the protein structure/function. We interpret G546S as a variant of uncertain significance. |
Labcorp Genetics |
RCV001222225 | SCV001394318 | uncertain significance | Fanconi anemia | 2022-10-26 | criteria provided, single submitter | clinical testing | This sequence change replaces glycine, which is neutral and non-polar, with serine, which is neutral and polar, at codon 546 of the FANCM protein (p.Gly546Ser). This variant is present in population databases (rs768676143, gnomAD 0.009%). This variant has not been reported in the literature in individuals affected with FANCM-related conditions. ClinVar contains an entry for this variant (Variation ID: 373472). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV002481278 | SCV002786535 | uncertain significance | Spermatogenic failure 28; Premature ovarian failure 15 | 2022-01-18 | criteria provided, single submitter | clinical testing |