Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000804844 | SCV000944777 | uncertain significance | Fanconi anemia | 2022-01-08 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The glutamine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. ClinVar contains an entry for this variant (Variation ID: 649821). This variant has not been reported in the literature in individuals affected with FANCM-related conditions. This variant is present in population databases (rs763495035, gnomAD 0.004%). This sequence change replaces arginine, which is basic and polar, with glutamine, which is neutral and polar, at codon 658 of the FANCM protein (p.Arg658Gln). |
Fulgent Genetics, |
RCV002487719 | SCV002789283 | uncertain significance | Spermatogenic failure 28; Premature ovarian failure 15 | 2021-12-15 | criteria provided, single submitter | clinical testing |