Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001349240 | SCV001543574 | uncertain significance | Fanconi anemia | 2020-03-01 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The serine amino acid residue is found in multiple mammalian species, suggesting that this missense change does not adversely affect protein function. These predictions have not been confirmed by published functional studies and their clinical significance is uncertain. This variant has not been reported in the literature in individuals with FANCM-related conditions. This variant is present in population databases (rs775175323, ExAC 0.02%). This sequence change replaces asparagine with serine at codon 950 of the FANCM protein (p.Asn950Ser). The asparagine residue is weakly conserved and there is a small physicochemical difference between asparagine and serine. |
Gene |
RCV001773698 | SCV002003183 | uncertain significance | not provided | 2024-02-12 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Fulgent Genetics, |
RCV002476607 | SCV002781339 | uncertain significance | Spermatogenic failure 28; Premature ovarian failure 15 | 2022-05-30 | criteria provided, single submitter | clinical testing |