Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001822551 | SCV002065326 | uncertain significance | not specified | 2021-06-07 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001869761 | SCV002207897 | uncertain significance | Fanconi anemia | 2021-06-06 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals with FANCM-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change replaces tryptophan with cysteine at codon 12 of the FANCM protein (p.Trp12Cys). The tryptophan residue is moderately conserved and there is a large physicochemical difference between tryptophan and cysteine. |