Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV000534630 | SCV000658025 | uncertain significance | Charcot-Marie-Tooth disease type 4 | 2018-11-29 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine with cysteine at codon 1380 of the PRX protein (p.Arg1380Cys). The arginine residue is moderately conserved and there is a large physicochemical difference between arginine and cysteine. This variant is present in population databases (rs771840476, ExAC 0.006%). This variant has been reported in an individual affected with chemotherapy-induced peripheral neuropathy (PMID: 25164601). Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C15"). In summary, this variant is a rare missense change with uncertain impact on protein function. It has been classified as a Variant of Uncertain Significance. |
Molecular Genetics Laboratory, |
RCV000790183 | SCV001336156 | uncertain significance | Charcot-Marie-Tooth disease | criteria provided, single submitter | clinical testing | ||
Inherited Neuropathy Consortium | RCV000790183 | SCV000929574 | uncertain significance | Charcot-Marie-Tooth disease | no assertion criteria provided | literature only |