Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002398461 | SCV002709710 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-05-18 | criteria provided, single submitter | clinical testing | The p.C531Y variant (also known as c.1592G>A), located in coding exon 8 of the RET gene, results from a G to A substitution at nucleotide position 1592. The cysteine at codon 531 is replaced by tyrosine, an amino acid with highly dissimilar properties. This amino acid position is well conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Baylor Genetics | RCV003464527 | SCV004208692 | uncertain significance | Hirschsprung disease, susceptibility to, 1 | 2023-09-04 | criteria provided, single submitter | clinical testing |