Total submissions: 11
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000409467 | SCV000489827 | benign | Multiple endocrine neoplasia type 2B | 2016-05-03 | criteria provided, single submitter | clinical testing | |
Counsyl | RCV000411041 | SCV000489828 | benign | Multiple endocrine neoplasia type 2A | 2016-05-03 | criteria provided, single submitter | clinical testing | |
ARUP Laboratories, |
RCV001002253 | SCV001160129 | likely benign | not specified | 2019-04-11 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV001102853 | SCV001259545 | benign | Pheochromocytoma | 2018-01-12 | criteria provided, single submitter | clinical testing | This variant was observed in the ICSL laboratory as part of a predisposition screen in an ostensibly healthy population. It had not been previously curated by ICSL or reported in the Human Gene Mutation Database (HGMD: prior to June 1st, 2018), and was therefore a candidate for classification through an automated scoring system. Utilizing variant allele frequency, disease prevalence and penetrance estimates, and inheritance mode, an automated score was calculated to assess if this variant is too frequent to cause the disease. Based on the score and internal cut-off values, a variant classified as benign is not then subjected to further curation. The score for this variant resulted in a classification of benign for this disease. |
Illumina Laboratory Services, |
RCV001102854 | SCV001259546 | uncertain significance | Renal hypodysplasia/aplasia 1 | 2018-01-12 | criteria provided, single submitter | clinical testing | This variant was observed in the ICSL laboratory as part of a predisposition screen in an ostensibly healthy population. It had not been previously curated by ICSL or reported in the Human Gene Mutation Database (HGMD: prior to June 1st, 2018), and was therefore a candidate for classification through an automated scoring system. Utilizing variant allele frequency, disease prevalence and penetrance estimates, and inheritance mode, an automated score was calculated to assess if this variant is too frequent to cause the disease. Based on the score, this variant could not be ruled out of causing disease and therefore its association with disease required further investigation. A literature search was performed for the gene, cDNA change, and amino acid change (if applicable). No publications were found based on this search. This variant was therefore classified as a variant of unknown significance for this disease. |
Illumina Laboratory Services, |
RCV001108068 | SCV001265263 | likely benign | Hirschsprung disease, susceptibility to, 1 | 2018-01-12 | criteria provided, single submitter | clinical testing | This variant was observed in the ICSL laboratory as part of a predisposition screen in an ostensibly healthy population. It had not been previously curated by ICSL or reported in the Human Gene Mutation Database (HGMD: prior to June 1st, 2018), and was therefore a candidate for classification through an automated scoring system. Utilizing variant allele frequency, disease prevalence and penetrance estimates, and inheritance mode, an automated score was calculated to assess if this variant is too frequent to cause the disease. Based on the score and internal cut-off values, a variant classified as likely benign is not then subjected to further curation. The score for this variant resulted in a classification of likely benign for this disease. |
Illumina Laboratory Services, |
RCV001108069 | SCV001265264 | benign | Multiple endocrine neoplasia | 2018-01-12 | criteria provided, single submitter | clinical testing | This variant was observed in the ICSL laboratory as part of a predisposition screen in an ostensibly healthy population. It had not been previously curated by ICSL or reported in the Human Gene Mutation Database (HGMD: prior to June 1st, 2018), and was therefore a candidate for classification through an automated scoring system. Utilizing variant allele frequency, disease prevalence and penetrance estimates, and inheritance mode, an automated score was calculated to assess if this variant is too frequent to cause the disease. Based on the score and internal cut-off values, a variant classified as benign is not then subjected to further curation. The score for this variant resulted in a classification of benign for this disease. |
Invitae | RCV002058857 | SCV002370422 | likely benign | Multiple endocrine neoplasia, type 2 | 2024-01-19 | criteria provided, single submitter | clinical testing | |
KCCC/NGS Laboratory, |
RCV000409467 | SCV004017353 | benign | Multiple endocrine neoplasia type 2B | 2023-07-07 | criteria provided, single submitter | clinical testing | |
Myriad Genetics, |
RCV000411041 | SCV004018055 | likely benign | Multiple endocrine neoplasia type 2A | 2023-04-17 | criteria provided, single submitter | clinical testing | This variant is considered likely benign. This variant is intronic and is not expected to impact mRNA splicing. |
All of Us Research Program, |
RCV002058857 | SCV004826179 | likely benign | Multiple endocrine neoplasia, type 2 | 2023-08-15 | criteria provided, single submitter | clinical testing |