Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001315295 | SCV001505864 | uncertain significance | Multiple endocrine neoplasia, type 2 | 2024-01-24 | criteria provided, single submitter | clinical testing | This variant, c.448_450del, results in the deletion of 1 amino acid(s) of the RET protein (p.Phe150del), but otherwise preserves the integrity of the reading frame. This variant is present in population databases (rs776989694, gnomAD 0.003%). This variant has not been reported in the literature in individuals affected with RET-related conditions. ClinVar contains an entry for this variant (Variation ID: 1016306). Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV002329267 | SCV002636973 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-03-11 | criteria provided, single submitter | clinical testing | The c.448_450delTTC variant (also known as p.F150del) is located in coding exon 3 of the RET gene. This variant results from an in-frame TTC deletion at nucleotide positions 448 to 450. This results in the in-frame deletion of a phenylalanine at codon 150. This amino acid position is poorly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive (Choi Y et al. PLoS ONE. 2012; 7(10):e46688). Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV002476466 | SCV002779656 | uncertain significance | Hirschsprung disease, susceptibility to, 1; Multiple endocrine neoplasia type 2B; Pheochromocytoma; Familial medullary thyroid carcinoma; Multiple endocrine neoplasia type 2A | 2022-05-16 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004590321 | SCV005081445 | uncertain significance | not provided | 2024-05-03 | criteria provided, single submitter | clinical testing | In-frame deletion of 1 amino acid in a non-repeat region; In silico analysis supports a deleterious effect on protein structure/function; Observed in an individual with Hirschsprung disease and exocrine pancreatic insufficiency (PMID: EelenJ2020[article]); Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 14633923, EelenJ2020[article]) |