Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000221001 | SCV000279605 | pathogenic | not provided | 2024-11-25 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect on ion channel function (PMID: 39021275); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis indicates that this missense variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 22526352, 36210150, 39021275) |
Inherited Neuropathy Consortium | RCV000789593 | SCV000928949 | uncertain significance | Neuronopathy, distal hereditary motor, autosomal dominant | no assertion criteria provided | literature only |